Abstract

Introduction: Langerhans cell histiocytosis is a rare multiorgan disorder, commonly seen in the pediatric age group. Commonest presentation of the disease involving the temporal bone is ear discharge. This entity is often underdiagnosed and the patient is treated with multiple courses of antibiotics which leads to delay in diagnosis and initiating apropriate treatment.

Case report: We present case reports of 2 children who presented to us with this rare disease. The line of management followed is discussed briefly. Our aim is to increase awareness of this disease amongst otolaryngologists and pediatricians so that they can identify such cases in a timely manner.

Conclusion: Langerhans cell histiocytosis can affect any age group but is commonly seen in children. It can involve any organ system but the temporal bone is involved in most cases. The differential diagnosis of this disease should be kept in mind for any patient presenting with chronic ear discharge that is not responding to the appropriate line of management.

Keywords

langerhans cell histiocytosis, temporal bone, ear discharge, otitis media