Abstract

Background:Herlyn Werner Wunderlich syndrome (HWWS) is a rare female urogenital tract abnormality, isolated by presenting a didelfous uterus, transverse vaginal septum and ipsilateral renal agenesis.
Objective: A case report of a patient with Werner Herlyn Wunderlich syndrome.
Case report:Female patient of 17 years of age, single, nubile, menarche at 14 years, infrequent menstrual cycles, normal volume, with dysmenorrhea EVA 7/10, attends to present disabling pelvic pain, ultrasound was found finding, hematocolpos and hematometra, is complemented with hysteroscopy, computed tomography (CT) and magnetic resonance imaging (MRI), a diagnosis of HWWS syndrome is integrated by confirming the presence of a didelfo uterus, obstructed right hemivagina and right renal agenesis, with distention of the vagina and cervix secondary to hematometra and hematocolpos, normal ovaries. The approach in this patient was by minimal invasion.
Conclusion: Herlyn Werner Wunderlich syndrome is a rare mullerian defect, it is often diagnosed late, the diagnosis is usually made after menarche, associated with chronic pelvic pain or palpable pelvic mass; 2D ultrasound along with physical examination performs the suspected diagnosis; This should be complemented with RM. The treatment of choice is vaginal septum resection assisted by minimally invasive techniques

Keywords

Herlyn Werner Wunderlich syndrome, uterus didelphys, renal agenesis, blind pouch, eutrophic cervix, endocervical canal, uterine cavity, unilateral renal agenesis, hematosalpinx, gynecologic endoscopy