Abstract

Subependymal giant cell astrocytomas (SEGAs) are WHO grade I tumors, most frequently associated with tuberous sclerosis complex (TSC). TSC sometimes also called Bourneville’s disease is a neurocutaneous disorder characterized by hamartoma of many organs like skin, brain, eye and kidneys. In this report, we illustrate the case of SEGA with hydrocephalus, who presented with features of raised intracranial pressure, along with shunt malfunction due to shunt valve blockage with proteinaceous material. Patient underwent interhemispheric transcallosal approach and complete removal of tumor followed by ventriculo- atrial shunt and achieved favourable outcome.

Keywords

Tuberous sclerosis complex, subependymal nodules, cerebrospinal fluid, hyperproteinorrhachia