Abstract

Our report describes a child with sickle-cell anemia presenting with left-sidedperiorbital swelling, headache, elevated leukocytes and inflammatory markers, discovered to have orbital bone infarction. Initial treatment included antibiotics for presumed infection. As MRI orbit suggested infarction of the orbital bone, exchange transfusion and steroid course was administered with subsequent improvement of symptoms. This case demonstrates that although infectionisa more common etiology of periorbital edema in sickle-cell disease, maintaining the differential of orbital bone infarction is crucial as patient out comes depend on prompt intervention. Caution is advised when treating these patients with steroids given risk of rebound pain.

Keywords

pediatrics, hematology, sickle cell anemia, orbital complication, vaso occlusive crisis, orbital bone infarction