Abstract

Hyper IgE syndrome is a rare primary immunodeficiency disease characterized by pruritic dermatitis, recurrent cutaneous abscesses, recurrent sinopulmonary infections and extremely elevated levels of IgE in serum. Although various systemic findings have been identified in hyper-IgEsyndome, renal disease is rarely associated with it. Here we report a rare case of a three years old child with hyper-IgE syndrome who had developed nephrotic syndrome.

Keywords

otitis media, mucocutaneous candidiasis, spongiosis, perivascular dermatitis, otitis media, mucocutaneous candidiasis, spongiosis, perivascular dermatitis