Abstract

Pansclerotic morphea is a highly rare, treatment-resistant, and debilitating variant of localized morphea that affects the entire thickness of the skin and sometimes involves muscles and bone. It manifests as expanding sclerotic plaques that eventually coalesce over the whole trunk or circumferentially extend into the extremities. It is also associated with an increased risk of cutaneous squamous cell carcinoma. Herein, we present the first case of a 30-year-old male patient with typical features of pansclerotic morphea in Yemen. Our patient’s case is unique because it presents a new sign not reported before, namely the boxer-jump sign, besides other previously reported typical signs.

Keywords

pansclerotic morphea, plaques, localized scleroderma, tip-toe gait, top tank sign, boxer-jump sign